ISSN 1308-7649 | E-ISSN 2148-3817
Case Report
“Emergency” Cochlear Implantation in Labyrinthitis Ossificans Secondary to Polyarteritis Nodosa: How to Face a Rare Entity
1 Department of Otolaryngology, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy  
2 Department of Experimental Medicine, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy  
3 Department of Rheumatology, University of Pavia, IRCCS Policlinico "S. Matteo" Foundation, Pavia, Italy  
J Int Adv Otol ; : -
DOI: 10.5152/iao.2018.5463
Key Words: Polyarteritis nodosa, cochlear implant, sudden sensorineural hearing loss, labyrinthitis ossificans
Abstract

Polyarteritis nodosa (PAN) is a systemic vasculitis affecting the small- and medium-sized arteries that may present with hearing impairment. In rare cases, PAN may be associated with progressive labyrinthitis ossificans (LO), an otologic emergency requiring early cochlear implantation (CI) to restore hearing before the complete, irreversible cochlear ossification. We report the first case in the literature of a patient affected by PAN with bilateral sudden sensorineural hearing loss and rapid LO who underwent “emergency” bilateral simultaneous CI. This case report emphasizes the importance of an early audiological evaluation in patients with PAN when LO is suspected. Multidisciplinary approach is mandatory when facing organ-specific manifestations in patients with PAN. Detailed discussion is provided with particular regard to clinical and radiological presentation as well as CI outcomes in such a rare and challenging case.


Cite this article as
: Canzi P, Aprile F, Manfrin M, Avato I, Magnetto M, Minervini D, et al. “Emergency” Cochlear Implantation in Labyrinthitis Ossificans Secondary to Polyarteritis Nodosa: How to Face a Rare Entity. J Int Adv Otol 2018. DOI: 10.5152/iao.2018.5463.

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