The Journal of International
Advanced Otology
Review

Chondromyxoid Fibroma of the Mastoid: A Rare Entity with Comprehensive Literature Review

1.

Department of Otorhinolaryngology, Al-Azhar University, Cairo, Egypt

2.

Department of Otorhinolaryngology, University Medical Center Utrecht, Utrecht, Netherlands

3.

Department of Pathology, University Medical Center Utrecht, Utrecht, Netherlands

4.

Department of Otorhinolaryngology, University Hospital Antwerp, University of Antwerp, Antwerp, Belgium

J Int Adv Otol 2020; 16: 117-122
DOI: 10.5152/iao.2019.6911
Read: 317 Downloads: 170 Published: 01 April 2020

Chondromyxoid fibroma (CMF) is the least commonly occurring bone tumor of cartilaginous origin. It is usually situated in the metaphysis of long bones of the lower limbs. Localization of the tumor in the skull is extremely rare. The definitive diagnosis is challenging and depends on radiological and histological examinations. To the best of our knowledge, only 14 cases of CMF involving the temporal bone have been reported to date, 7 of which were within the mastoid. The most common clinical symptom is headache; however, these symptoms vary greatly according to site, size, and extension of the lesion. Surgical removal is the treatment of choice. A literature review of the diagnostic challenges, histological difficulties in differential diagnosis, imaging, clinical features, and recommended modalities of treatment have been discussed in the present case.Chondromyxoid fibroma (CMF) is the least commonly occurring bone tumor of cartilaginous origin. It is usually situated in the metaphysis of long bones of the lower limbs. Localization of the tumor in the skull is extremely rare. The definitive diagnosis is challenging and depends on radiological and histological examinations. To the best of our knowledge, only 14 cases of CMF involving the temporal bone have been reported to date, 7 of which were within the mastoid. The most common clinical symptom is headache; however, these symptoms vary greatly according to site, size, and extension of the lesion. Surgical removal is the treatment of choice. A literature review of the diagnostic challenges, histological difficulties in differential diagnosis, imaging, clinical features, and recommended modalities of treatment have been discussed in the present case.

Cite this article as: Elsamanody A, Van den Aardweg M, Smits A, Willems S, Topsakal V. Chondromyxoid Fibroma of the Mastoid: A Rare Entity with Comprehensive Literature Review. J Int Adv Otol 2020; 16(1): 117-22.

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