The Journal of International
Advanced Otology
Case Report

Intracochlear Vestibular Schwannoma Presenting with Mixed Hearing Loss


Department of Otorhinolaryngology-Head and Neck Surgery and Audiology, Rigshospitalet, University Hospital of Copenhagen, Denmark


Faculty of Health and Medical Sciences, University of Copenhagen, Copenhagen, Denmark

J Int Adv Otol 2021; 17: 265-268
DOI: 10.5152/iao.2021.8586
Read: 1318 Downloads: 521 Published: 01 May 2021

As for other vestibular schwannomas, intralabyrinthine schwannomas commonly cause a sensorineural hearing loss, contrary to more lateral ear pathology that can cause conductive or mixed hearing loss. This case report features a patient that presented with a mixed and thus partly pseudo-conductive hearing loss due to an intracochlear schwannoma, a finding that is very rare. As a result, the patient was initially misdiagnosed as having otosclerosis and a stapedotomy was performed, without hearing improvement. We discuss the clinical implications of this atypical presentation, which illustrates the importance of performing supplementary audiological testing (e.g., the Gellé test), and the importance of considering vestibular system testing when otosclerosis is suspected. In addition, the importance of imaging and considering differential diagnoses in cases of conductive hearing loss is stressed.

Cite this article as: Diana Reda J, West N, Cayé-Thomasen P. Intracochlear vestibular schwannoma presenting with mixed hearing loss. J Int Adv Otol. 2021;17(3):265-268.

EISSN 2148-3817