Parachordoma is a rare soft tissue mixed tumor, associated with soft tissue myoepithelioma. It is typically growing slowly and considered less aggressive than other similar soft tissue tumors. However, it does recur sporadically, and on rare occasions, it has demonstrated the ability to metastasize. Although imaging is important, definitive diagnosis is achieved by histology, and it is typically treated by a wide local excision. We present the first reported case of a skull base parachordoma in a 15-year-old boy, managed with a wide local excision and with no signs of recurrence or metastases after 24 months of follow-up.
Cite this article as: de Cates C, Borsetto D, Scoffings D, O’Donovan D, Donnelly N. Skull Base Parachordoma / Myoepithelioma. J Int Adv Otol 2020; 16(2): 278-81.