ISSN 1308-7649 | E-ISSN 2148-3817
Original Article
Cochlear Implantation Outcomes in Children with Agenesis of the Corpus Callosum: A Retrospective Study and A Review of the Literature
1 Department of Otorhinolaryngology Head & Neck Surgery, Çukurova University School of Medicine, Adana, Turkey  
J Int Adv Otol ; : -
DOI: 10.5152/iao.2019.6577
Key Words: cochlear implant, corpus callosum, agenesis, auditory performance

OBJECTIVES: The aim of this study was to analyze the outcomes of cochlear implantation in patients with agenesis of the corpus callosum (CCA). A literature review and retrospective analysis of our cochlear implant database were carried out.


MATERIALS AND METHODS: To the best of our knowledge, in the literature in English, there was only one case reported with the CCA that had undergone cochlear implantation surgery. This case had the Donnai Barrow Syndrome. In our database, of the 1317 patients who underwent cochlear implantation surgery, five patients who had CCA were selected. The patients’ demographic characteristics, operative findings, surgical outcome and additional disabilities were investigated. The patients’ preoperative and postoperative listening progress profile (LiP) and meaningful auditory integration scale (MAIS) tests were done to analyze the auditory performances.


RESULTS: The participants of the study were 5 individuals (0.38 %) (2 male and 3 female patients; ages, 5.5, 7.5, 8, 9 and 12 years). Two of the patients had total agenesis, and the other three had partial agenesis of the corpus callosum. In the histories of the patients, one patient had parental consanguinity and one had febrile convulsion. No patient had an additional disability. None had experienced device failure. No patients were non-users or limited users of cochlear implants. Postoperative LiP and MAIS test scores were improved for all patients nearly as the patients without any deformity. They showed normal auditory performance in the analysis in their postoperative 48th-month follow-up.


CONCLUSION: The patients who had CCA are good candidates for cochlear implantation surgery.


Cite this article as: Özdemir S, Tuncer Ü, Sürmelioğlu Ö, Tarkan Ö, Çetik F, Kıroğlu M, et al. Cochlear Implantation Outcomes in Children with Agenesis of the Corpus Callosum: A Retrospective Study and A Review of the Literature. J Int Adv Otol 2019; 10.5152/iao.2019.6577.

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