The Journal of International Advanced Otology
Case Report

Axial Mesodermal Dysplasia Complex with a Unique Abnormal Course of Vestibulocochlear Nerve

1.

Department of Radiology, Mersin University School of Medicine, Mersin, Turkey

2.

Department of Otolaryngology-Head and Neck Surgery, Mersin University School of Medicine, Mersin, Turkey

3.

Department of Pediatrics, Mersin University School of Medicine, Mersin, Turkey

J Int Adv Otol 2019; 15: 317-320
DOI: 10.5152/iao.2018.5830
Read: 19 Downloads: 6 Published: 03 September 2019

Abstract

 

Axial mesodermal dysplasia complex (AMDC) is a combination of multiple congenital malformations arising due to the mesodermal cell migration, neural tube fusion, and rhombencephalon segmentation. Here, we present the imaging findings of a 15-year-old boy with AMDC who has bilateral inner ear malformations associated with a vestibulocochlear nerve extending to Meckel cave, cystic lesion in prepontine cisterna, cervical vertebral segmentation anomalies, and maxillar bone anomalies.

 

Cite this article as: Tok Umay S, Özgür A, Görür K, Kömür M, Balcı Y. Axial Mesodermal Dysplasia Complex with a Unique Abnormal Course of Vestibulocochlear Nerve. J Int Adv Otol 2019; 15(2): 317-20.

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ISSN1308-7649 EISSN 2148-3817