Abstract

Axial mesodermal dysplasia complex (AMDC) is a combination of multiple congenital malformations arising due to the mesodermal cell migration, neural tube fusion, and rhombencephalon segmentation. Here, we present the imaging findings of a 15-year-old boy with AMDC who has bilateral inner ear malformations associated with a vestibulocochlear nerve extending to Meckel cave, cystic lesion in prepontine cisterna, cervical vertebral segmentation anomalies, and maxillar bone anomalies.

Cite this article as: Tok Umay S, Özgür A, Görür K, Kömür M, Balcı Y. Axial Mesodermal Dysplasia Complex with a Unique Abnormal Course of Vestibulocochlear Nerve. J Int Adv Otol 2019; 15(2): 317-20.